BACKGROUNDS. Esophageal atresia encompasses a group of congenital anomalies comprising of an interruption of continuity of the esophagus, usually with a persistent communication with the trachea – tracheoesophageal fistula. Anatomical classification is used to describe various types of atresia. Newborns with esophageal atresia usually present with frothing, coughing, choking and regurgitation following feeding attempts. The diagnosis of esophageal atresia is established by passing a nasogastric tube and meeting resistance at the end of a blind esophageal pouch or the tube may also become coiled in the esophagus, which can be confirmed by chest x-ray. Newborns with esophageal atresia should be stabilized and then transferred in incubator to the surgical center. Other congenital anomalies are also frequently associated with esophageal atresia. The management of esophageal atresia is surgical. The survival rates of low risk newborns in developed centers are close to 100%. METHODS. A retrospective analysis was done of all newborns that were operated on because of esophageal atresia between the years 2004 and 2010 and were hospitalized at the Intensive Care Unit of the Department of Paediatric Surgery and Intensive Care of the Ljubljana University Medical Centre. RESULTS. In 7 years, 34 newborns with esophageal atresia were admitted and operated. During surgery, the following variants were found: esophageal atresia with distal tracheoesophageal fistula, esophageal atresia with proximal and distal tracheoesophageal fistula, esophageal atresia with proximal tracheoesophageal fistula, isolated esophageal atresia, and isolated tracheoesophageal fistula. Thirty newborns survived till discharge and 4 died. CONCLUSIONS. The incidence of esophageal atresia in Slovenia is in accordance with published data. A higher incidence of esophageal atresia with proximal and distal tracheoesophageal fistula as well as a high proportion of coarctation of the aorta among newborns with associated anomalies were noticed. The type of surgical repair done at our hospital is similar to the treatmeat in other centers, although a higher proportion of newborns in which additional surgery was needed was noticed. The survival of newborns with esophageal atresia in Slovenia is compatible to survival rates reported by other centers.