Acute hepatic porphyrias are rare disorders of heme metabolism and can potentially be let­hal. Diagnosis is based on the clinical presentation and laboratory analysis of urine. Adequate and early treatment can prevent further complications. The paper presents a case of a 30-year-old patient with known diabetes mellitus, who had several episodes of abdomi­nal pain over the past three years. During his second hospitalization, acute hepatic porphyria was diagnosed, which was probably due to hypoglycemia and psychological stress. After sympto­matic treatment, the patient was discharged with detailed instructions on the factors which may precipitate acute attacks. Upon the outpatient control examination, the patient had no symptoms or clinical or laboratory signs of porphyria. Acute hepatic porphyria is often mis­sed. Normoglycemic patients with diabetes mellitus can have other precipitating factors. Education of patients and prevention of precipitating factors can prevent acute attacks.